Pulmonary Arterial Hypertension (PAH)


Pulmonary arterial hypertension (PAH) is continuous high blood pressure in the pulmonary artery. The average blood pressure in a normal pulmonary artery is about 14 mmHg when the person is resting. In PAH, the average is usually greater than 25 mmHg. PAH is a serious condition for which there are beneficial treatments, but no cure.

There are two types of PAH:

  • Primary pulmonary arterial hypertension (PPAH)- inherited or occurs for no known reason.
  • Secondary pulmonary arterial hypertension (SPAH)- caused by or occurs because of another condition. The conditions include chronic heart or lung disease, blood clots in the lungs, or a disease like scleroderma.



Resources

Pulmonary Hypertension Association www.phassociation.org
PHCentral www.phcentral.org




Drug Information

The following drugs are FDA-approved for the treatment of PAH.

Tracleer www.tracleer.com
Letairis www.letairis.com
Ventavis www.4ventavis.com
Remodulin www.remodulin.com
Flolan www.gsk.com
Revatio www.revatio.com
Adcirca www.adcirca.com
Tyvaso www.tyvaso.com